Cerebellar Ataxia – Disease Knowledge Hub

Clinical Rating Scales

Scale for the Assessment and Rating of Ataxia (SARA)

Guidelines

Management of the Ataxias: Towards Best Clinical Practice
Consensus Clinical Management Guidelines for Friedreich’s Ataxia (2022)

Diagnosis

Diagnostic Flowchart for Adult Ataxias (new version 09/2024)
Diagnostic Flowchart for Early-Onset Ataxias

Information for Patients – Endorsed by ERN-RND

General Ataxia Leaflet (provided by Ataxia UK)
Muscle Tightness & Stiffness – ‘Spasticity’ in Ataxia
Friedreich’s Ataxia

Patient information leaflet – FA in 13-17 years old adolescents

Patient information leaflet – FA in 4-12 years old children

Hereditary Spastic Paraplegias (HSPs) – Disease Knowledge

Clinical Rating Scales

The Spastic Paraplegias Rating Scale (SPRS)
Scales to measure HSP in children before adolescence

Diagnosis

Diagnostic flowchart for Hereditary Spastic Paraplegias (HSPs)