Cerebellar Ataxia & Hereditary Spastic Paraplegias (HSPs)

About the Page
The Cerebellar Ataxia & Hereditary Spastic Paraplegias Disease Knowledge Page provides reference information on care of cerebellar ataxia and hereditary spastic paraplegias.

Information and knowledge that has been developed or endorsed by ERN-RND is found in the blue boxes.

Care Standards - Clinical Rating Scales

Ataxias:

Scale for the assessment and rating of ataxia (SARA)


Hereditary Spastic Paraplegias:

The Spastic Paraplegias Rating Scale (SPRS)

Scales to measure HSP in children before adolescence

Care Standards - Guidelines

Ataxias:

Management of the ataxias: towards best clinical practice

Consensus clinical management guidelines for Friedreich’s Ataxia

Care Standards - Diagnosis

Ataxias:
Diagnostic flowchart for Ataxia (new version 09/2024, updating translations)

Diagnostic flowchart for early-onset Ataxias


Hereditary Spastic Paraplegias:
Diagnostic flowchart for Hereditary Spastic Paraplegias (HSPs)

Patient Journey

Ataxias:
Patient Journey Friedreich's Ataxia


Hereditary Spastic Paraplegias:
Patient Journey Hereditary Spastic Paraplegias (HSPs)

Information for patients - endorsed by ERN-RND

Ataxia:
General Ataxia leaflet (provided by Ataxia UK):

Muscle tightness & stiffness - 'spasticity' in Ataxia

Friedreich's Ataxia:
Patient information leaflet - FA in 13-17 years old adolescents

Patient information leaflet - FA in 4-12 years old children

Patient registries to which ERN-RND members contribute

Patient information

Please note that this section includes useful information from a variety of sources provided by ERN-RND members but which hasn’t been endorsed by ERN-RND.

Further useful links, training resources, evidence and publications

Publications